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KMID : 0882420140860010096
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Korean Journal of Medicine
2014 Volume.86 No. 1 p.96 ~ p.101
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Malignant Perivascular Epithelioid Cell Tumor (PEComa) Arising in the Omentum with Metastatic Peritoneal Seeding: A Case Report
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Jang Suk-Bin
Suh Won-Yong
Jeon Ji-Hyun
Park Keon-Woo
Lim Do-Hyoung
Namgung Hwan
Lee Soon-Il
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Abstract
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The World Health Organization (WHO) defines a perivascular epithelioid cell tumor (PEComa) as a mesenchymal neoplasia composed of perivascular epithelioid cells with characteristic morphological and immunohistochemical features. They are rarely malignant. Indeed, only a few cases have been reported in the English literature, and this is the first case of PEComa reported in Korea. A 64-year-old man presented with an abdominal mass and peritoneal seeding. The patient underwent mass excision with descending colon resection and anastomosis. The primary mass and peritoneal seeding was diagnosed as a PEComa histopathologically. Seven months later, he developed liver metastasis and aggravated peritoneal seeding. Here, we report a case of malignant PEComa of the omentum.
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KEYWORD
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Perivascular epithelioid cell neoplasms, HMB-45 protein
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